{"id":33781,"date":"2015-07-23T11:47:19","date_gmt":"2015-07-23T10:47:19","guid":{"rendered":"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/?p=33781"},"modified":"2015-07-23T22:05:24","modified_gmt":"2015-07-23T21:05:24","slug":"sindrome-de-poland","status":"publish","type":"post","link":"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/sindrome-de-poland\/","title":{"rendered":"S\u00edndrome de Poland"},"content":{"rendered":"<h1 style=\"text-align: left;\"><\/h1>\n<h1 style=\"text-align: left;\"><strong>S\u00edndrome de Poland<\/strong><\/h1>\n<p style=\"text-align: justify;\"><strong>Resumen<\/strong><\/p>\n<p style=\"text-align: justify;\">El s\u00edndrome de Poland se caracteriza por la ausencia total o parcial del m\u00fasculo pectoral mayor, con un grado variable de anomal\u00edas de la mano del mismo lado y que puede tener asociadas otras malformaciones. Es un s\u00edndrome espor\u00e1dico, cuya causa exacta se desconoce, aunque parece corresponder a una alteraci\u00f3n vascular del mesodermo que afecta a la arteria clavicular. La asociaci\u00f3n en miembros de la misma familia se ha descrito en casos aislados.<\/p>\n<p style=\"text-align: justify;\"><!--more--><\/p>\n<p style=\"text-align: justify;\"><strong>S\u00edndrome de Poland<\/strong><\/p>\n<ul>\n<li style=\"text-align: justify;\">TERD Susana Comino Martinez<\/li>\n<li style=\"text-align: justify;\">TERD \u00c1ngela L\u00f3pez Grandio<\/li>\n<li style=\"text-align: justify;\">TERD Eva Rovira Alonso<\/li>\n<\/ul>\n<p style=\"text-align: justify;\">Palabras clave: s\u00edndrome de Poland, anomal\u00eda, musculo pectoral, malformaci\u00f3n, t\u00f3rax.<\/p>\n<p style=\"text-align: justify;\"><strong>Presentaci\u00f3n del caso <\/strong><\/p>\n<p style=\"text-align: justify;\">Paciente de 6 a\u00f1os de edad con sintomatolog\u00eda de tos y fiebre de varios d\u00edas de evoluci\u00f3n, en la historia cl\u00ednica podemos observar que tiene una malformaci\u00f3n osteomuscular cong\u00e9nita detectada a los pocos d\u00edas de nacer.<\/p>\n<p style=\"text-align: justify;\">Podemos ver en dos radiograf\u00edas de t\u00f3rax una del 2013 (figura1 y figura 2) y otra del 2015 (figura\u00a03 y figura 4) la paciente diagnosticada de s\u00edndrome de Poland (deformidad de la caja tor\u00e1cica proximal izquierda, ausencia del m\u00fasculo pectoral izquierdo). Tambi\u00e9n podemos detectar una dextrocardia y una desalineaci\u00f3n de la columna dorsal.<\/p>\n<p style=\"text-align: justify;\">Figura 1<\/p>\n<figure id=\"attachment_33782\" aria-describedby=\"caption-attachment-33782\" style=\"width: 390px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/1-s\u00edndrome-de-Poland.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33782\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/1-s\u00edndrome-de-Poland.jpg\" alt=\"s\u00edndrome-de-Poland\" width=\"400\" height=\"287\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/1-s\u00edndrome-de-Poland.jpg 400w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/1-s\u00edndrome-de-Poland-300x215.jpg 300w\" sizes=\"auto, (max-width: 400px) 100vw, 400px\" \/><\/a><figcaption id=\"caption-attachment-33782\" class=\"wp-caption-text\">S\u00edndrome de Poland<\/figcaption><\/figure>\n<p style=\"text-align: justify;\">Figura 2<\/p>\n<figure id=\"attachment_33783\" aria-describedby=\"caption-attachment-33783\" style=\"width: 390px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/2-s\u00edndrome-de-Poland-radiografia.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33783\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/2-s\u00edndrome-de-Poland-radiografia.jpg\" alt=\"s\u00edndrome-de-Poland-radiografia\" width=\"400\" height=\"444\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/2-s\u00edndrome-de-Poland-radiografia.jpg 400w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/2-s\u00edndrome-de-Poland-radiografia-270x300.jpg 270w\" sizes=\"auto, (max-width: 400px) 100vw, 400px\" \/><\/a><figcaption id=\"caption-attachment-33783\" class=\"wp-caption-text\">S\u00edndrome de Poland. Radiograf\u00eda<\/figcaption><\/figure>\n<p style=\"text-align: justify;\">Figura 3<\/p>\n<figure id=\"attachment_33784\" aria-describedby=\"caption-attachment-33784\" style=\"width: 390px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/3-s\u00edndrome-de-Poland-radiografia-torax.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33784\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/3-s\u00edndrome-de-Poland-radiografia-torax.jpg\" alt=\"s\u00edndrome-de-Poland-radiografia-torax\" width=\"400\" height=\"332\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/3-s\u00edndrome-de-Poland-radiografia-torax.jpg 400w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/3-s\u00edndrome-de-Poland-radiografia-torax-300x249.jpg 300w\" sizes=\"auto, (max-width: 400px) 100vw, 400px\" \/><\/a><figcaption id=\"caption-attachment-33784\" class=\"wp-caption-text\">S\u00edndrome de Poland. Radiograf\u00eda de t\u00f3rax<\/figcaption><\/figure>\n<p style=\"text-align: justify;\">Figura 4<\/p>\n<figure id=\"attachment_33785\" aria-describedby=\"caption-attachment-33785\" style=\"width: 390px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/4-Poland-deformidad-caja-toracica.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33785\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/4-Poland-deformidad-caja-toracica.jpg\" alt=\"Poland-deformidad-caja-toracica\" width=\"400\" height=\"315\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/4-Poland-deformidad-caja-toracica.jpg 400w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/4-Poland-deformidad-caja-toracica-300x236.jpg 300w\" sizes=\"auto, (max-width: 400px) 100vw, 400px\" \/><\/a><figcaption id=\"caption-attachment-33785\" class=\"wp-caption-text\">Poland. Deformidad de la caja tor\u00e1cica<\/figcaption><\/figure>\n<p style=\"text-align: justify;\"><strong>DISCUSI\u00d3N <\/strong><\/p>\n<p style=\"text-align: justify;\">El s\u00edndrome de Poland de car\u00e1cter raro y cong\u00e9nito en el que se ve afectado el desarrollo muscular su nombre es en honor a Alfred Poland que lo descubri\u00f3 en 1841 al realizar una autopsia mientras era estudiante. Frecuencia 1 de cada 30.000 nacidos vivos.<\/p>\n<p style=\"text-align: justify;\">Es un defecto de nacimiento raro caracterizado por el subdesarrollo o ausencia del m\u00fasculo pectoral mayor en un lado del cuerpo y de la mano en el mismo lado, principalmente com\u00fan al lado derecho del cuerpo, pero como es nuestro caso tambi\u00e9n puede ser el izquierdo. Es m\u00e1s frecuente en hombres que en mujeres.<\/p>\n<p style=\"text-align: justify;\"><!--nextpage--><\/p>\n<p style=\"text-align: justify;\">Durante la exhalaci\u00f3n y la inspiraci\u00f3n parte del pulm\u00f3n sobresale a trav\u00e9s de la zona afectada por la ausencia de cart\u00edlagos y costillas. Los ni\u00f1os presentan catarros cr\u00f3nicos y como es normal problemas psicol\u00f3gicos.<\/p>\n<p style=\"text-align: justify;\">El tratamiento es en principio quir\u00fargico, antes de la operaci\u00f3n estos pacientes deben ser controlados cada seis meses debido a problemas pulmonares y para prevenir deformaciones de columna por la fragilidad de la estructura tor\u00e1cica.<\/p>\n<p style=\"text-align: justify;\">No existe patr\u00f3n de herencia ni factores de riesgo conocidos hasta el momento.<\/p>\n<p style=\"text-align: justify;\">DIAGRAMA MUSCULAR<\/p>\n<figure id=\"attachment_33786\" aria-describedby=\"caption-attachment-33786\" style=\"width: 360px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/5-s\u00edndrome-de-Poland-musculos.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33786\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/5-s\u00edndrome-de-Poland-musculos.jpg\" alt=\"s\u00edndrome-de-Poland-musculos\" width=\"370\" height=\"148\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/5-s\u00edndrome-de-Poland-musculos.jpg 370w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/5-s\u00edndrome-de-Poland-musculos-300x120.jpg 300w\" sizes=\"auto, (max-width: 370px) 100vw, 370px\" \/><\/a><figcaption id=\"caption-attachment-33786\" class=\"wp-caption-text\">S\u00edndrome de Poland. M\u00fasculos<\/figcaption><\/figure>\n<p style=\"text-align: justify;\">AUSENCIA DE MAMA Y PECTORAL<\/p>\n<figure id=\"attachment_33787\" aria-describedby=\"caption-attachment-33787\" style=\"width: 360px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/6-s\u00edndrome-de-Poland-ausencia-mama.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33787\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/6-s\u00edndrome-de-Poland-ausencia-mama.jpg\" alt=\"s\u00edndrome-de-Poland-ausencia-mama\" width=\"370\" height=\"148\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/6-s\u00edndrome-de-Poland-ausencia-mama.jpg 370w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/6-s\u00edndrome-de-Poland-ausencia-mama-300x120.jpg 300w\" sizes=\"auto, (max-width: 370px) 100vw, 370px\" \/><\/a><figcaption id=\"caption-attachment-33787\" class=\"wp-caption-text\">S\u00edndrome de Poland. Ausencia de mama<\/figcaption><\/figure>\n<p style=\"text-align: justify;\">AUSENCIA DE PECTORAL MAYOR Y MENOR<\/p>\n<figure id=\"attachment_33788\" aria-describedby=\"caption-attachment-33788\" style=\"width: 360px\" class=\"wp-caption aligncenter\"><a href=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/7-s\u00edndrome-de-Poland-ausencia-pectoral.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"size-full wp-image-33788\" src=\"http:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/7-s\u00edndrome-de-Poland-ausencia-pectoral.jpg\" alt=\"s\u00edndrome-de-Poland-ausencia-pectoral\" width=\"370\" height=\"148\" srcset=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/7-s\u00edndrome-de-Poland-ausencia-pectoral.jpg 370w, https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/7-s\u00edndrome-de-Poland-ausencia-pectoral-300x120.jpg 300w\" sizes=\"auto, (max-width: 370px) 100vw, 370px\" \/><\/a><figcaption id=\"caption-attachment-33788\" class=\"wp-caption-text\">S\u00edndrome de Poland. Ausencia de pectoral<\/figcaption><\/figure>\n<p style=\"text-align: justify;\"><strong>BIBLIOGRAF\u00cdA<\/strong><\/p>\n<p style=\"text-align: justify;\">&#8211; Burkhardt H, Buss J. Dextrocardia and Poland syndrome in a 59-year-old patient. Z Kardiol. 1997;86:639-43.<\/p>\n<p style=\"text-align: justify;\">&#8211; P\u00e9rez Belmonte E, Ochoa Sangrador C, Marug\u00e1n Isabel V, Casanueva Pascual T, Carrascal Tejado A. Secuencia de Poland y dextrocardia. An Pediatr (Barc). 2004;61:350-1.<\/p>\n<p style=\"text-align: justify;\">&#8211; Cruz M, Bosch J. Hipoplasia. Agenesia del m\u00fasculo pectoral con sindactilia (Poland). En: Cruz M, Bosch J, editores. Atlas de s\u00edndromes pedi\u00e1tricos. Barcelona: Espaxs; 1998.<\/p>\n<p style=\"text-align: justify;\">&#8211; www.enfermedades-raras.org<\/p>\n<p style=\"text-align: justify;\">&#8211; Jones, KL, s\u00edndrome de Poland en: Atlas de Malformaciones Cong\u00e9nitas 4\u00aa Edici\u00f3n interamericana, M\u00e9xico 1990.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>S\u00edndrome de Poland Resumen El s\u00edndrome de Poland se caracteriza por la ausencia total o parcial del m\u00fasculo pectoral mayor, con un grado variable de anomal\u00edas de la mano del mismo lado y que puede tener asociadas otras malformaciones. Es un s\u00edndrome espor\u00e1dico, cuya causa exacta se desconoce, aunque parece corresponder a una alteraci\u00f3n vascular &#8230; <\/p>\n<p class=\"read-more-container\"><a title=\"S\u00edndrome de Poland\" class=\"read-more button\" href=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/sindrome-de-poland\/#more-33781\" aria-label=\"Leer m\u00e1s sobre S\u00edndrome de Poland\">Leer m\u00e1s<\/a><\/p>\n","protected":false},"author":2,"featured_media":33789,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[184],"tags":[6147,6149,6148,6146,6150],"class_list":["post-33781","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-pediatria-neonatologia","tag-anomalia","tag-malformacion","tag-musculo-pectoral","tag-sindrome-de-poland","tag-torax","no-featured-image-padding"],"acf":[],"yoast_head":"<!-- This site is optimized with 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