{"id":53774,"date":"2019-11-27T11:07:20","date_gmt":"2019-11-27T10:07:20","guid":{"rendered":"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/?p=53774"},"modified":"2019-11-27T11:07:34","modified_gmt":"2019-11-27T10:07:34","slug":"schwannoma-del-septum-nasal-a-proposito-de-un-caso","status":"publish","type":"post","link":"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/schwannoma-del-septum-nasal-a-proposito-de-un-caso\/","title":{"rendered":"Schwannoma\u00a0 del\u00a0 septum\u00a0 nasal. A prop\u00f3sito de un caso"},"content":{"rendered":"<p style=\"text-align: justify;\"><strong>Schwannoma\u00a0 del\u00a0 septum\u00a0 nasal. A prop\u00f3sito de un caso<\/strong><\/p>\n<p style=\"text-align: justify;\">Los tumores de origen neur\u00f3geno representan el 3% de los tumores nasales. Dentro de estos los schawnnomas son poco usuales, benignos y de localizaci\u00f3n m\u00e1s frecuente en cabeza y cuello y extremidades. La localizaci\u00f3n en tabique nasal es extraordinariamente rara.<!--more--><\/p>\n<p style=\"text-align: justify;\"><strong>Paula Milena Casallas Austin. M\u00e9dico especialista en Otorrinolaringolog\u00eda. Servicio de otorrinolaringolog\u00eda del Complejo hospitalario de Navarra. Pamplona, Espa\u00f1a.<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>Resumen:<\/strong><\/p>\n<p style=\"text-align: justify;\">Los tumores de origen neur\u00f3geno representan el 3% de los tumores nasales. Dentro de estos los schawnnomas son poco usuales, benignos y de localizaci\u00f3n m\u00e1s frecuente en cabeza y cuello y extremidades. La localizaci\u00f3n en tabique nasal es extraordinariamente rara.<\/p>\n<p style=\"text-align: justify;\">El diagn\u00f3stico definitivo se realiza mediante estudio anatomopatol\u00f3gico utilizando la prote\u00edna S100. El tratamiento de elecci\u00f3n es la extirpaci\u00f3n quir\u00fargica, donde la TAC y RMN resultan \u00fatiles para planear el abordaje quir\u00fargico m\u00e1s adecuado.<\/p>\n<p style=\"text-align: justify;\">Neurogenic tumors represent 3% of nasal tumors. Within these schawnnomas are unusual, benign and more frequent in the head and neck and extremities. The nasal septum location is extraordinarily rare.<\/p>\n<p style=\"text-align: justify;\">The definitive diagnosis is made by pathological study using the S100 protein. The treatment of choice is surgical removal, where CT and MRI are useful for planning the most appropriate surgical approach.<\/p>\n<p style=\"text-align: justify;\">Palabras clave:<\/p>\n<p style=\"text-align: justify;\">Schwannoma del septum nasal, septum nasal, schwannoma, tumores nasosinusales, cirug\u00eda endosc\u00f3pica nasal.<\/p>\n<p style=\"text-align: justify;\">nasal septal schwannoma; nasal septal; schwannoma; sinonasal tumour; transnasal endoscopic surgery<\/p>\n<p style=\"text-align: justify;\"><strong><u>Introducci\u00f3n<\/u><\/strong><\/p>\n<p style=\"text-align: justify;\">Los tumores de origen neur\u00f3geno representan el 3% de los tumores nasales. Dentro de estos los schawnnomas son poco usuales, benignos y de localizaci\u00f3n mas frecuente en cabeza y cuello y extremidades. La localizaci\u00f3n en tabique nasal es extraordinariamente rara.<\/p>\n<p style=\"text-align: justify;\">Presentamos el 2\u00ba caso de este tumor en septum nasal en edad pedi\u00e1trica tras el publicado por Soy en 1950.<\/p>\n<p style=\"text-align: justify;\"><strong><u>Caso cl\u00ednico<\/u><\/strong><\/p>\n<p style=\"text-align: justify;\">Paciente de 12 a\u00f1os que acude a nuestra consulta por cuadro de obstrucci\u00f3n nasal izquierda de semanas de evoluci\u00f3n sin otra sintomatolog\u00eda asociada. Mediante rinoscopia anterior se observa una tumoraci\u00f3n que ocupa la totalidad del vest\u00edbulo, desplaza el tabique y produce deformidad est\u00e9tica a nivel alar. (Imagen 1)<\/p>\n<p style=\"text-align: justify;\">El TAC describe lesi\u00f3n redondeada con densidad homog\u00e9nea y ligeramente hipodensa de 2 cm de di\u00e1metro m\u00e1ximo en la parte m\u00e1s anterior del vest\u00edbulo nasal izquierdo, dependiente del tercio anterior del septum. (Imagen 2)<\/p>\n<p style=\"text-align: justify;\">Se decide biopsia-ex\u00e9resis en quir\u00f3fano, extirp\u00e1ndose por v\u00eda endonasal una tumoraci\u00f3n de consistencia firme, color viol\u00e1ceo de 2 x 1 cm, con base de implantaci\u00f3n en tercio anterior de tabique nasal. ( Imagen 3)<\/p>\n<p style=\"text-align: justify;\">El informe anatomopat\u00f3l\u00f3gico describe proliferaci\u00f3n fusocelular con patr\u00f3n de crecimiento nodular. C\u00e9lulas con n\u00facleo elongado y citoplasma mal delimitado (c\u00e9lulas Antoni A).Disposici\u00f3n celular en empalizada rodeando un estroma hialino (Cuerpos de Verocay). Pruebas inmunohistoqu\u00edmicas positiva para Prote\u00edna S-100, espec\u00edfica de schawnnoma.<\/p>\n<p style=\"text-align: justify;\">La paciente presenta una evoluci\u00f3n satisfactoria y tras 10 a\u00f1os, no ha presentado recidiva.<\/p>\n<p style=\"text-align: justify;\"><strong><u>Conclusiones:<\/u><\/strong><\/p>\n<p style=\"text-align: justify;\">El schwannoma de septum es una entidad rara, benigna, sin s\u00edntomas caracter\u00edsticos, siendo su malignizaci\u00f3n excepcional. El diagn\u00f3stico definitivo se realiza mediante estudio anatomopatol\u00f3gico utilizando la prote\u00edna S-100.<\/p>\n<p style=\"text-align: justify;\">El tratamiento de elecci\u00f3n es la extirpaci\u00f3n quir\u00fargica de la totalidad de la masa, para evitar una posible recidiva, previo estudio con TAC y\/o RMN para descartar otras lesiones.<\/p>\n<p style=\"text-align: justify;\"><iframe style=\"width: 100%; height: 500px;\" src=\"http:\/\/docs.google.com\/gview?url=https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/SCHWANNOMA-DE-SEPTUM-NASAL.pdf&amp;embedded=true\" frameborder=\"0\"><\/iframe><a href=\"https:\/\/www.revista-portalesmedicos.com\/revista-medica\/wp-content\/uploads\/SCHWANNOMA-DE-SEPTUM-NASAL.pdf\">SCHWANNOMA-DE-SEPTUM-NASAL<\/a><\/p>\n<p style=\"text-align: justify;\"><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li style=\"text-align: justify;\">Min HJ, Hong SC, Kim KS. Nasal Septal Schwannoma: Advances in Diagnosis and Treatment. J Craniofac Surg. 2017 Jan;28(1):e97-e101.<\/li>\n<li style=\"text-align: justify;\">Min HJ, Kim KS. Differential Diagnosis Between Nasal Septal Schwannoma and Nasal Septal Neurofibroma. J Craniofac Surg. 2017 Oct;28(7):1780-1783.<\/li>\n<li style=\"text-align: justify;\">Chou MS, Chung HK, Tsou YA, Chen JJ, Tsai MH, Jan CI. Endoscopic management of pediatric sinonasal schwannoma: case report. B-ENT. 2014;10(4):299-302.<\/li>\n<\/ol>\n","protected":false},"excerpt":{"rendered":"<p>Schwannoma\u00a0 del\u00a0 septum\u00a0 nasal. A prop\u00f3sito de un caso Los tumores de origen neur\u00f3geno representan el 3% de los tumores nasales. Dentro de estos los schawnnomas son poco usuales, benignos y de localizaci\u00f3n m\u00e1s frecuente en cabeza y cuello y extremidades. La localizaci\u00f3n en tabique nasal es extraordinariamente rara.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[180],"tags":[12351,2737,12348,12349,12350],"class_list":["post-53774","post","type-post","status-publish","format-standard","hentry","category-otorrinolaringologia","tag-cirugia-endoscopica-nasal","tag-schwannoma","tag-schwannoma-del-septum-nasal","tag-septum-nasal","tag-tumores-nasosinusales","no-featured-image-padding"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Schwannoma\u00a0 del\u00a0 septum\u00a0 nasal. A prop\u00f3sito de un caso<\/title>\n<meta name=\"description\" content=\"Schwannoma\u00a0 del\u00a0 septum\u00a0 nasal. 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